Bicoronal Suture Synostosis (Syndromic)
Premature closure of both coronal sutures, usually associated with genetic syndromes such as Apert, Crouzon and Pfeiffer syndrome.
- Normal head contour
- Prematurely fused suture
- Compensatory growth
Bicoronal Suture Synostosis (Syndromic Synostosis)
Bicoronal suture synostosis occurs when both coronal sutures of the skull (the seams running over the ears) close prematurely, either before birth or shortly after. The head may take on a widened appearance (similar to brachycephaly), and the forehead may look flattened.
Syndromic Association
Bicoronal synostosis is frequently seen together with genetic syndromes such as Apert syndrome, Crouzon syndrome, Pfeiffer syndrome and Saethre-Chotzen syndrome. These syndromes may be accompanied by anomalies of the hands, feet and face. A multidisciplinary evaluation (genetics, neurosurgery, pediatrics) is required.
Evaluation
Diagnosis is made through physical examination, 3D imaging (CT), genetic testing and assessment by a specialist team. The treatment plan is tailored individually to each patient's clinical picture.
Important Note
This page is for general information only and does not replace a medical diagnosis. Please be sure to have your baby's condition assessed by your specialist doctor.
